Case Number : Case 2263 - 14 February 2019 Posted By: Raul Perret

Submucosal vascular lesion with anastomosing lymphatic chanels lined by prominent endothelial cells which are not very atypical, focal intraluminal papillary proliferation is noted. I think it is  benign lymphangioendothelioma(old term APL). multiple lesions can happen with thrombocytopenia which can result severe bleeding. Not kaposi to me.

I like Henry's comment. No inflammatory infiltrate, no hemosiderin, intraluminal papillary projections and promontory sign are in keeping with Lymphangioendothelioma...but last two pics are reminiscent of Hemangioblastoma.Im not familiar with extracerebellar hemangioblastomas. So this is a puzzle case for me. 

What about Glial (whit pseudovascular configuration) and meningeal (last two pictures) heterotopia?

I remember a similar case here: Case Number : Case 1564 - 23 June

Lymphangioendothelioma (progressive lymphangioma) is a great thought. Also see case 2244.

6 hours ago, Alex-Ventura-Leon said:

What about Glial (whit pseudovascular configuration) and meningeal (last two pictures) heterotopia?

I remember a similar case here: Case Number : Case 1564 - 23 June

That is a brilliant idea. I did note those last two images resembling glial tissue.. bravo!

Congrats to Alex. Great idea!!!

If in the scalp, it could be a meningothelial hamartoma/choristoma of Suster... In the gum it could be a glial and meningeal heterotopia...But histology is more in keeping with Suster's tumor. I don't know.

Meningeothelial heterotopia

I called this extracranial meningioma/meningothelial heteropia. The dissecting/pseudovascular pattern has been more frequently described in meningothelial heteropia but whether this lesions represent hamartomas or true neoplasms is controversial.